Usher syndrome is a genetic disorder that is characterized by complications in vision and hearing; the most common of them being partial/complete loss of hearing and retinitis pigmentosa. Retinitis pigmentosa is characterized by progressive deterioration of the retina, resulting in deprivation of peripheral vision and subsequent night blindness.

The symptoms and its rate of progression usually vary among people. Usher syndrome is classified into three types:

Type 1: In this type, children are born with balance issues and hearing loss problems. The symptoms of night blindness and loss of peripheral vision associated with  Retinitis Pigmentosa  only appear in the early stages of adolescence.
Type 2: In type 2, children are born with moderate to mild hearing loss problems. Retinitis Pigmentosa develops soon after the child reaches adolescence.
Type 3: In type 3 Usher Syndrome, children are usually born with normal hearing skills, however, loss of hearing and Retinitis pigmentosa occur soon after puberty.
Causes
Hearing loss in Usher syndrome occurs when the nerve cells that are present in the cochlear (inner ear s spiral cavity) are affected by genetic mutation. A similar problem occurs in the cells of the retina leading to loss of vision. These cells allow conversion of light into electrical signals for the brain to interpret them. Both the parents need to pass the mutated gene to the child for it to be affected. If the child has only one gene, then he/she rarely develops the symptoms.

Treatment
This disorder does not have any prescribed course of treatments. The vision loss that occurs in this disorder can be slowed down by nutritional therapy. This therapy involves providing the body with essential amounts of vitamin A which can help in reducing vision loss.

Usher Syndrome - Things You Must Know!

A deaf child is the one who suffers from hearing loss. Children with deafness may also fail to develop speech. Such children might have no defect in their speech but they cannot speak anything. The main reason is deafness. They do not hear a speech, therefore, cannot develop it. Deafness may not be hereditary, but it occurs due to several other causes. 

The period of 5 years is crucial in a child s life. During this period, they develop their speech and language. Therefore, parents need to take the utmost care for the early identification of hearing loss and treat the child accordingly. 

Causes of Deafness in Children

There are several causes of deafness in children.

Otitis Media: In young children, if the eustachian tube is not fully formed, it forms fluid behind the eardrum. This fluid can get infected and affect the hearing. The fluid may not cause any pain or infection but still, it can harm and cause hearing loss even if it stays for a short time. 

Problems by Birth: Some children have hearing problems by birth. Sometimes, the problem lies in the genes. But, other times during pregnancy or prenatal care, the problem arises. If a mother, while pregnancy, has diabetes or preeclampsia, she is likely to deliver a deaf child. A prematurely born baby also has a high risk of deafness.

Illness or Injury: Some young children suffer hearing loss due to some injury in the ear or some other illness. Illness includes meningitis, measles, chickenpox, and flu. Head injury or listening to loud music for a long time can also be a reason.

Symptoms of a Deaf Child

A deaf child shows no reaction to the loud noises.

He/she doesn t respond to the voices.

The sound of the child is simple that taper off.

The child may pull or rub the ear several times, which is noticeable.

The child is continuously cranky for no particular reason.

He/she does not pay any attention when anyone is talking.

He/she has very little energy to do anything. 

He/she fails to understand the direction.

Often asks to raise the volume of TV or radio.

Have fever and ear pain.

Treatment of the Problem

Hearing loss affects a child s learning ability. So, the problem must be diagnosed and treated immediately. Here are some treatment approaches: 

Treatment for Otitis Media: The very first thing parents and doctors can do is watchful waiting because sometimes the problem cures itself. Some pediatricians might prescribe some antibiotics. If the problems continue, then the doctor will suggest getting an ear tube to the child that will allow the fluid to drain. For this, the child will have to visit an ENT doctor also called Otolaryngologist. 

Treatment for other causes: The child may use a hearing aid. Some can get cochlear implants. 

Conclusion
It is necessary for parents to accept the child with deformity and stay by his/her side. They must get themselves educated and communicate the problem with others to get help. It is essential to stay in touch with the child and take care of him.

Deaf Child - What Should You Know?

You should consider undertaking a cochlear implant in case you are experiencing hearing loss or are turning deaf. This is a small device that gets planted in your ear through a surgical procedure. It sends impulses to your auditory nerves directly, as a result of which sound signals get carried to your brain. Cochlear implants may not make you hear normally again, but help you with different sounds, and in the recognition of the different sounds around you like alarms, telephones, and door bells.

How it works?

A cochlear implant is fit for children and adults who suffer from the sensorineural hearing loss. This condition damages the tiny hair cells in your inner ear, which is called the cochlea. Hearing becomes impaired when these get damaged.
The device consists of two specific parts. The first part or the receiver-stimulator is placed under your skin via a surgical procedure. The other part of the device is the speech processor. It has to be worn around your neck in the form of a hearing aid.
The external device is, however, larger in size than a usual hearing aid. The receiver gets placed under your skin, behind the ear via a small incision. It is connected to electrodes.
This is inserted into the cochlea of your inner ear. The surgery requires a few hours to be undertaken successfully.
The speech processor has to be placed two weeks after the surgery is undertaken. The processor can be connected to the microphone, and this can be worn around the ear.
You can wear it on any other part of your body, based on your lifestyle and age.
Benefits of cochlear implant
The major benefits of a cochlear implant are as follows:

You might be able to hear speech almost normally.
You will be able to understand speech better, and will not have to depend on lip reading.
It will be much easier and simpler for you to listen to the television and talk over the phone.
You will be able to listen to music better.
You may also be able to pick up various sounds around you that include soft, medium, and loud sounds.
You will be able to control your own voice better. This makes other people understand you better.
If you are suffering from severe hearing loss, a cochlear implant may be able to change your life for the better. However, the results are not the same for all, and vary among people. It is possible for some people to benefit more from such an implant than others. 

Cochlear Implants - 6 Benefits You Must Know!

Hearing loss is not something limited to elderly men or elderly women only. This is something that can affect any adult at any stage of life. The good news is that it can be managed. Today, there are a number of hearing aids that can help improve hearing ability. These aids allow an individual who has lost part of his or her hearing to live a normal life. For best results, hearing loss should be arrested in its early stages.

Here are a few signs you should look out for.

Muffled Speech: When you hear people talk, their speech should be clearly identifiable. If you hear muffled noises that you have to interpret as words, it could be a sign of hearing loss.
Difficulty understanding words: The human ear has the ability to separate conversational sounds from ambient noise. However, in some cases where the inner ear is damaged, a person might find it difficult to separate the two. In such cases, the person might not be able to understand words clearly as they get confused with background noise. This is a sign that must never be taken lightly.
Feeling the need to ask people to repeat themselves: Once in a while if you find yourself asking another person to repeat what he or she said, there is nothing to worry. However, if this becomes a regular occurrence and happens with many people, then the fault lies in your hearing. Thus, if you notice yourself needing to ask people to repeat themselves or talk slowly, consult a hearing specialist.
Increasing the volume of the radio or television: As children, we are taught that playing music or watching TV at a very high volume can damage the ears. The radio, television and other such appliances should be played at a volume where the information being relayed is clearly audible and people can have a conversation alongside without needing to shout. If you find yourself having to increase the volume constantly, it could be a sign of hearing loss.
Withdrawing from conversations: As hearing loss is aggravated, people begin to feel conscious of having to ask others around them to repeat themselves or talk slowly. This can make them withdraw from a conversation and other social situations. In many cases, the simple reason for avoiding a party could be the discomfort of not being able to hear the other person clearly in a conversation.
 All hearing problems can be better handled by proper investigation, different test, sign and symptoms of the patient, which are carried by a specialist of hearing, called as AUDIOLOGIST, who can look your hearing problems, plan out treatment plan, rehabilitation pre and post etc. Audiologist will definitely help you hear again. 

Common Signs Of Hearing Problems In Adults!

You may find out that your child is suffering from hearing loss when he is born or he may be diagnosed with the condition later in life. Hearing loss in children is commonly caused by otitis media, birth problems and on the account of certain injuries or illnesses.

Signs and symptoms

The early-stage symptoms of hearing loss in children are as follows:

No reaction to extremely loud noises

No response or reaction to your voice

The child makes some sounds, which taper off

The other symptoms which follow include:

He may pull and rub his ears.

He may act cranky constantly without any proper reason.

He might stop paying attention.

Low energy levels are indicated.

He may find it hard to follow directions.

He may ask you to increase the volume of the radio or TV.

Fever and ear pain are also likely symptoms.

Treatment

Early hearing loss can affect a child s language learning skills. If the problem is diagnosed and treated soon, the problem with language can be avoided. The method of treatment depends on the cause of hearing loss in your child and the severity of hearing loss.

There are certain medicines for hearing---prescribed by your ENT Surgeon. Please take the point watchful waiting. Even, if you have the slightest doubt of hearing loss contact ENT immediately.

The primary treatment methods of hearing loss in children include the following:

Watchful waiting: Sometimes, the condition may resolve on its own and the treatment involves simple monitoring of your child for positive changes.

Medicines: There are certain medicines for hearing loss in children, which may be prescribed by your pediatrician.

Ear tubes: Ear tubes may be recommended if medicines and monitoring do not work. The tubes allow fluid to drain and help in preventing infections. A minor surgery has to be undertaken on your child for getting the ear tubes placed. This will solve hearing loss and other related issues.

Hearing aids: Hearing aids may be used to allow your child to hear better. It is safe for children to use ear tubes after the age of one month. For the right hearing aid for your child, you need to consult a hearing specialist.

Implants: Cochlear implants are used to treat hearing loss in many children. These are electronic devices that are put in the inner ear to benefit hearing. These should be used only if hearing aids did not succeed and these are meant to be used only in the case of children with serious hearing problems.

There are several other devices, which can help your child with hearing loss. For suggestions and recommendations, you must take your child to a hearing specialist.

Hearing Loss In Children - Signs And Treatment Of It!

It is that time of the year when insects are all around. Suddenly one feels a buzzing sound or an itchy feel in the ear. To your horror, one feels a live insect is in your ear, which can be extremely annoying and is like a nightmare. Insects often get stuck when they enter our ears as they cannot fly or crawl out. They try to find their way out and their movements inside our ears can be very uncomfortable, painful and can be itchy as well. Moreover, they can easily produce infection.

In this scenario, do not try to remove an insect with cotton swab, tweezers or hair clip as it will make the situation worse and can lodge the insect deeper into the ear canal, which can possibly damag the eardrum, leading to permanent hearing loss. If an individual is not certain about the potential harm taht can be caused by the insect in the ear, one should seek medical care immediately. Insects in the ear are common reasons for visits to doctor's clinic, especially in children.

If one suspects an insect in ear, one may experience pain, swelling, blood or crackling. One may even feel biting, stinging, hearing loss or dizziness. It is best to stay calm in this situation as being active may lodge the bug further in ear or cause it to move further back or cause serious damage to the sensitive eardrum

One way to try to remove a bug in ear is by tilting the ear toward the ground and attempt to wiggle the ear. Grasp the earlobe and give it a wiggle. If the bug is not too far into ear canal, it may fall out on its own. If the bug is still alive and is not too far inside of the ear canal, it may simply come out on its own. If one stays calm and keep objects including fingers away from ears, it is likely that the bug will find its way back out of ear.

One can also try to flush the ear with warm water with a dropper or a bulb syringe. This can be done by holding head upright and stretching the ear canal by pulling the outer ear and then putting a steady stream of warm water into ear. Tilt head to the side to drain out the ear. Do not try this if one suspects that ear drum has been ruptured to prevent additional damage.

To avoid stinging or eardrum rupture from scratching or biting , one may use a drop or two of mineral, baby, or olive oil inside your ear canal to kill the insect. Finally, visit an ENT specialist doctor as they can remove the insect by special suction devices. Post insect removal, one must look out for signs of infection as swelling, dizziness, hearing loss, fever, and pain. Finally follow up with ENT specialist or Otolaryngologist for the final opinion.

How to Remove Insect from Ear at Home? 

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