Cystic Fibrosis is a genetic disorder that is known to affect some of the vital organs of the body including the lungs, digestive system to name a few. For long it was believed that cystic fibrosis affects a person in their childhood. However, various research and studies suggest that adults are also susceptible to this inheritable disorder. In this article, we will discuss the cause and symptoms associated with cystic fibrosis.

Cause
The epithelial cells that line the stomach, nasal cavity and lungs, are responsible for the production of the digestive fluids, sweat, tears, mucus. The Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) gene codes for a protein called the CFTR protein. The CFTR protein, a membrane protein plays a pivotal role in transporting the chloride ions of the epithelial cells inside and out of the cell. This regulation of the chloride ions goes a long way in ensuring that the mucus produced is free-flowing and thin.

In the case of Cystic Fibrosis, the CFTR gene that codes for the protein undergoes a mutation. With the CFTR protein unable to perform its function, sticky and thick mucus builds up and clogs some of the major systems of the body including the digestive system, reproductive, and respiratory system. There is also a higher salt content in the sweat of the affected person.

For a person to be affected by cystic fibrosis, he/she must inherit a copy of the mutated CFTR gene from both the parents ( Autosomal Recessive Disorder) at birth.

Symptoms
The symptoms associated with cystic fibrosis depends on the organs and systems affected.

The thick mucus formed can clog the digestive tract resulting in incomplete absorption of the essential nutrients from the food. This may have an impact on the overall growth and development of the body.
- There may be stunted growth or no weight gain.
- The stool may appear greasy and foul smelling. Some may also suffer from constipation.
- Newborns and infants may suffer from an intestinal blockage.
Cystic fibrosis, left unattended can lead to diabetes, intestinal blockage or obstruction.
- The mucus can also block the bile duct triggering a host of problems including liver disorders.
- At times, the obstruction or blockage can occur at the junction where the large and the small intestine meets (Distal intestinal obstruction syndrome).
The thick mucus can also affect the lungs and the respiratory system by blocking the tubes that act as a passage carrying the air inside and out of the lungs. As a result,
- A person may suffer from lung infections frequently.
- There may be difficulty in breathing, stuffy and blocked nose, or wheezing.
- Some people may also suffer from a chronic cough with a thick sputum.
Left untreated the complications can worsen resulting in

Nasal polyps, Chronic infections, Hemoptysis (there is blood while coughing), and Pneumothorax (air fills up in the space bifurcates the chest wall from the lungs).

In severe cases, there may be a respiratory failure.

Cystic fibrosis can also trigger fertility problems (both in males and females).

Cystic Fibrosis- Causes and Symptoms!

When blood clot blocks one or more arteries in your lungs the condition is known as pulmonary embolism. It can cause a decrease in the oxygen levels in your blood, damage to your lungs due to sudden restrictions in the flow of blood along with adverse effects on other parts of your body. Life threatening blockage can cause death if left untreated and you should immediately contact your health care provider to get proper diagnosis. Pulmonary embolism requires various lab tests and generally requires short time to resolve.

Symptoms:
The symptoms of pulmonary embolism mainly depend upon many factors pertaining to your previous medical history. Pulmonary embolism varies with the size of your lungs, the size of the clots formed in your blood, and any other underlying history of the heart or lungs. That said, pulmonary embolism has symptoms which are not similar to any two persons and will vary accordingly.

The common symptoms however may include the following and you are advised to opt for a health checkup if these are persistent in your body:
1. Cough along with bloody sputum is a common symptom.
2. Shortness of breath, which will become worse as the days passes by. They will appear suddenly and cause huge discomfort in breathing.
3. Chest pain which may give you the feeling of a heart attack. The pain will intensify when you sit to eat or cough. Deep breath will cause problems too and will not go away easily with exertion.
4. Some other symptoms include fever, excess sweat, irregular heartbeat and dizziness.

Pulmonary embolism can be diagnosed by the following methods:
1. Electrocardiography (also known popularly as ECG) to measure your heart's electrical activity and functioning.
2. CT plumonary angiography is gold standard for diagnosing pulmonary embolism.
3. Chest x ray, which is a common and non invasive test to check your heart and lungs as well as the problems with any bones surrounding them.
4. ECHO can detect secondary changes in heart due to pulmonary embolism.

Treatment of pulmonary embolism can be done with medicines if it is detected at an early stage or also if the clot is small. However, if the size of your clot is problematic and blocks the blood flow to your lungs or heart then surgery may be necessary. Open surgery and clot removal surgery are common in the treatment of pulmonary embolism and will require good regular follow up check ups. Regular leg exercises will also reduce the chances of any underlying disease and you should hence consult your doctor.

What Is Pulmonary Embolism?

Without our lungs, it would be impossible to breathe. People suffering from chronic lung diseases have compromised lung functioning. This leads to shortness of breath, fatigue and weakness. In turn, this can make the person avoid anything that exerts the lungs such as exercise. While this may seem like a good idea, it is actually detrimental. Not exercising can further weaken the lungs and muscles and make this a vicious cycle. This is where physiotherapy can help with lung rehabilitation or pulmonary rehabilitation.

Physiotherapy is a branch of medicine that treats diseases and health conditions with exercise and manual therapy. Physiotherapists may also use radiation, sound waves, electric therapy, prosthesis and assistive devices. The aim here is not to cure the disease but to improve lung functioning and the patient s quality of life. Pulmonary rehabilitation can help in a number of ways.

It reduces breathlessness: As the lung muscles weaken, their ability to pump oxygen and transport it to the other parts of the body reduces. This can make a person feel breathless even with the slightest exertion. Lung rehabilitation works on strengthening the lung muscles to reduce this breathlessness.
It increases muscle strength in the arms and legs: When oxygen does not reach the limbs, they, in turn, get weaker. By strengthening the lungs, lung rehabilitation increases the muscle strength in the patient s arms and legs.
It increases stamina and endurance: Stamina is directly linked to lung functioning. By helping the patient breathe more comfortably, lung rehabilitation increases the patient s stamina and helps him or her endure more physical exercise.
It helps patients understand your condition: Physiotherapy is part exercise and part education. By helping patients get an insight into their condition, physiotherapy helps them come to terms with their limitations and motivates them to work harder towards overcoming them.
It increases self-confidence: Feeling breathless and tired all the time can make people feel frustrated. This is especially so because these things cannot be controlled without help. Physiotherapy teaches patients how to deal with these issues and thus increases their confidence in dealing with their medical issues.
It makes patients more independent: A lack of energy can make people dependent on others. Even simple tasks like getting a bottle of water from the fridge can seem like a tiring task. Physiotherapy improves lung functioning and hence makes the person feel less tired doing everyday tasks. This makes the person more independent and improves their quality of life.

Lung Rehabilitation With Physiotherapy!

Asthma is a condition that can flare up anytime; be it at your child's soccer practice or during the middle of the night. Whenever the condition sets in, it leads to your child struggling for breath. For a parent to witness this situation can be hard; but you should know the techniques to keep the situation under control.

Here are a few tips on how to manage the situation:

1. Find out the triggers in your home: Asthma is triggered due to substances that your child may be allergic to. Examples are cigarette smoke, fur of pets and dust. If possible, keep your child away from the known triggers so that the condition does not flare up again.

2. Keep records of the following: It is good to have an action plan ready for your child when the bouts of asthma strike. When you visit the doctor to discuss about your child's condition then make sure that you have these records at hand.

The triggers that caused the bout of asthma
How many times did your child have wheezing episodes?
The number of times your child has been admitted for the same reason
The medications that your child is currently taking, dosage and/or whether they have been changed
How often does he/she need medications if he/she has acute symptoms?
3. Knowledge of the test your child may require: Asthma control test is a type of test that allows parents and children to grade asthma symptoms without a doctor. A pulmonary function test is used to detect the capacity of the lungs and flow of air.

4. See how your child responds to the treatments: You should consider changing the treatments for your child if he/she has recurrent symptoms of asthma attack and require frequent visits to the Emergency Room even after taking medications for an extended duration.

5. Long term treatment plans require patience: Any asthma treatment plan requires patience as they might not immediately cure symptoms.

How to Manage if Your Child Is Suffering From Asthma

Air pollution is known to take a toll on the lungs of even the healthiest adults. So, it comes as no surprise that the effects of this pollution on the lungs of children is deemed as a grave situation, full of health hazards including the onset of Chronic Obstructive Pulmonary Disorders and conditions like asthma and other lung disorders. Read on to find out more about the link between air pollution and its effect on the lungs of children.

Children's Lungs: Mostly, all the organs of a child's body are considered delicate and not fully matured until the child reaches a certain age. The main and largest part of the child's lungs will usually grow only after the child is born, much like the arms and legs. In fact, it is a medically proven fact that about 80% of the tiniest of air sacs grow after the child's birth, these are called the alveoli and they facilitate the transfer of the oxygen into the bloodstream with a life-sustaining function that is built into our lungs. These alveoli continue to grow until the child becomes an adult. 

Immunity and Infections: Like the lungs of the child, the immunity of the child is also still in its growth phase, and is very much, unlike the immunity that an adult enjoys. This makes the child more susceptible to infections that are usually carried by air pollution in today's day and age of urban living when myriad pollutants are sent into the air every single day. Also, since children play outdoors more often and spend more time breathing in this air, they are more prone to these infections and lung or respiratory ailments due to this reason. Various studies and tests have shown inflammation in the respiratory passages caused by deposits of carbon dioxide emissions in the lungs of children.

Symptoms: Usually, the very first symptoms that show that air pollution is affecting your child's lungs can be seen when persistent coughing and wheezing sets in, without any proper reason. Also, when the child faces bronchial infections time and time again, all these are indicators of hazardous effects of air pollution in children.

Respiratory problems: Apart from respiratory problems, which can lead to asthmatic attacks, hay fever and allergies as well as other COPD ailments, there are other related dangers as well. These can happen when constant choking and obstruction of oxygen due to pollution becomes a regular affair. These include stroke and brain damage which can eventually also lead to a higher risk of dementia. 

How can you protect your child during such times?

Restrict outdoor activity for the time being, especially during the early morning and evening
Make sure that your child wears a face mask when outside, preferably N95 or 99
Use air purifiers at home 
Go green and use indoor plants that can remove indoor toxins
Boost your child's immunity
Lastly, keep a track of air quality index in your locality

Pollution - How It Can Affect Your Child's Lungs?

Asthma is a severe respiratory disease, which occurs due to the inflammation of the airways of lungs. The airways of the lungs get swollen due to the inflammation, which cause production of mucus. Due to the effect of excessive mucus and swelling, the air path gets hindered. In such a condition, breathing becomes difficult and a wheezing sound appears at the time of breathing. Usually, the patient coughs very often.

These are the common symptoms of asthma:

Breathlessness
Whistling sound while breathing
Wheezing in chest
Mucus-producing cough
Tightness and heaviness in breathing
Heaviness in chest while running, walking or performing any activity
Recommended homeopathic medicines
Homeopathy is the holistic way of treating asthma. It not only cuts down the inflammation, but also cures the cause of the inflammation. So, treating asthma with homeopathy is safe because the remedies are all natural. Homeopathic medicines do not produce any side effects. There are several homeopathic medicines which are used to treat mild or severe asthma. Here are the five best homeopathic remedies for asthma:

Arsenic album: Arsenic Album is one of the effective homeopathic medicines for the patients who have asthma with anxiety. The patient might encounter symptoms such as intense feeling of restlessness, intense wheezing and coughing, feeling of suffocation while lying down, sudden increase of thirst etc. Usually, patients get relief after consuming warm drinks.
Ipecac: This is one of the wonderful homeopathic medicines for treating asthma with intense vomiting and nausea. The patient might encounter symptoms such as vomiting along with asthma attacks, persistent nausea, intense feeling of mucus in the chest, persistent cough, persistent salivation etc. This medicine is generally prescribed to patients who are a little heavy in weight.
Antim tart: This is the best homeopathic remedy for asthma patients who have a rattling cough. The symptoms also include a feeling of mucus in the chest, sleepiness, tiredness etc. Also, there is usually a burning sensation in the chest and throat, intense cough after eating anything, breathlessness, and hoarseness of the voice. This is more common in older people.
Nux vomica: This is one of the best homeopathic remedies for patients who have asthma with the gastronomic disorder. Symptoms include feeling of fullness around the stomach with asthma attacks, dry cough, sensation in the throat, mood swings etc.
Carbo veg: This is one of the best homeopathic remedies for treating asthma patients with blueness on face. Symptoms include numbness in hands and feet, stomach problem, breathlessness while lying down etc.

Asthma - 5 Homeopathic Remedies That Can Really Do Wonders!

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