Usher syndrome is a genetic disorder that is characterized by complications in vision and hearing; the most common of them being partial/complete loss of hearing and retinitis pigmentosa. Retinitis pigmentosa is characterized by progressive deterioration of the retina, resulting in deprivation of peripheral vision and subsequent night blindness.

The symptoms and its rate of progression usually vary among people. Usher syndrome is classified into three types:

Type 1: In this type, children are born with balance issues and hearing loss problems. The symptoms of night blindness and loss of peripheral vision associated with  Retinitis Pigmentosa  only appear in the early stages of adolescence.
Type 2: In type 2, children are born with moderate to mild hearing loss problems. Retinitis Pigmentosa develops soon after the child reaches adolescence.
Type 3: In type 3 Usher Syndrome, children are usually born with normal hearing skills, however, loss of hearing and Retinitis pigmentosa occur soon after puberty.
Causes
Hearing loss in Usher syndrome occurs when the nerve cells that are present in the cochlear (inner ear s spiral cavity) are affected by genetic mutation. A similar problem occurs in the cells of the retina leading to loss of vision. These cells allow conversion of light into electrical signals for the brain to interpret them. Both the parents need to pass the mutated gene to the child for it to be affected. If the child has only one gene, then he/she rarely develops the symptoms.

Treatment
This disorder does not have any prescribed course of treatments. The vision loss that occurs in this disorder can be slowed down by nutritional therapy. This therapy involves providing the body with essential amounts of vitamin A which can help in reducing vision loss.

Usher Syndrome - Things You Must Know!

Proper and sound hearing is essential for a healthy living. If you are suffering from lack or loss of hearing, chances are that you are missing out on life itself. Therefore, it is imperative that you undergo ayurvedic treatments in case you are suffering from any kind of hearing ailment.

Common Cause of Loss of Hearing
There are various reasons that contribute to the loss of hearing. Some of the common causes are:

Age
Increasing noise
Genetically inherited
Over the years various surgical and non-surgical methods have surfaced that can help repair loss of hearing and damage. Among the other branches of medicines, some home remedies, and ayurvedic treatment for hearing loss and deafness.

Ayurvedic Remedies Fo Hear Loss
Ayurveda is the most old and ancient method. It uses natural herbs in order to correct and treat hearing loss. This has proved to be extremely beneficial and potent and it cures hearing ailments with the help of a number of natural home methods. Some of them are:

Lukewarm mustard oil or sesame oil: If you are suffering from ache in ears or loss in hearing, try putting few drops of warm mustard oil and sesame oil in your ear and hold it with index fingers. At the same time store air in your mouth and let your cheeks contract and bulge for a minute or so. This ayurvedic tip considerably improves hearing and reduces ear pain.
Radish juice and sesame oil: If you are suffering from sores and hearing problems, a mixture of the two can be beneficial. In this ayurvedic method, a small quantity of Radish juice should be boiled with a small quantity of sesame oil, till the juice absorbs the oil. This mixture should be administered twice a day in order to experience the results.
Applewood oil: A variety of ingredients are required in order to create the resultant oil. Initially, cow's urine should be boiled and the applewood powder must be added to it. This mixture should then be filtered and further added with sesame and goat's milk. This concoction is then boiled and the resultant oil should be stored and applied with cotton daily. This improves hearing a great deal.
A mixture of neem and turmeric: In this natural home remedy, turmeric and neem leaves are boiled together. The steam should be taken as well as the water must be applied to the ears and surrounding areas. This has proved to be an extremely effective remedy in treating pus in the ears and consequent hearing loss.
A mixture of Radish juice, turmeric, sesame oil, and ajwain seeds: All these ingredients must be taken in selective quantities and boiled to get the resultant oil. This oil must be stored and used to treat loss of hearing and other ear diseases.

5 Ayurvedic Tips To Improve Hearing

The sense of hearing is a complex one. The ears are divided into three parts: the outer ear, the middle ear and the inner ear. While the outer ear sends the sound to the middle of the ear, the middle ear sends the same to the inner ear through the conductor. The inner ear in turn sends the auditory signal to the brain where the signal is processed and gives rise to a sense of hearing. 

Problems in hearings can arise if there is a problem in any of these parts. However, more often than not it is the middle or inner ear that is affected. However, there may also be situations when there are problems in both the middle and the inner ear. In that case, it is known as a mixed hearing loss. 

What is Mixed Hearing? 

Loss If there is damage to the middle ear, it may precipitate a conductive hearing loss. Now, in addition to that, if there is a sensorineural problem, then it gives rise to mixed hearing. So, in the case of a mixed hearing loss, all the parts of the ear and even the brain may be involved. There may be damage to the outer ear, middle ear, inner ear, as well as the auditory nerve. 

Causes of Hearing Loss 

Since mixed hearing loss may result from damage to any part of the ear, it is necessary that the causes be grouped into different categories. 

  Sensorineural Hearing Loss 

Sensorineural loss may result from drugs, different illnesses, head trauma, malformation of the inner ear etc. Genetic predisposition may also precipitate such problems. 

  Conductive Hearing Loss 

Such type of hearing loss may result from excessive deposition of earwax, ear infections, perforation in eardrums, malformation of the middle or outer ear, as well as problems with the fluid in the middle ear. 

Symptoms of Hearing Loss 

Reduced hearing in either or both ears is considered to be delineating symptoms of mixed hearing loss. 

Treatment 

Since mixed hearing loss can result from sensorineural failure as well as damage to outer or middle ear, treatment needs to be divided into different groups too.   To treat Conductive Hearing Loss, doctors can use surgical or medical options. 

  For sensorineural hearing loss, doctors usually prescribe hearing aids. This indicates that treatment for mixed hearing loss may include treatment for conductive hearing loss as well as that for sensorineural hearing loss. So, it is usually a combination of both medical and surgical options. Physicians may prescribe both medicines and hearing aids or resort to surgical interventions and also prescribe hearing aids. Sometimes, physicians use special hearing aids or implants to treat mixed hearing loss. 

Conclusion 

In case a person is sensing reduced hearing in one or both ears, he/she needs to seek medical advice. It may be a symptom of mixed hearing loss. Getting in touch with an experienced physician is the first step towards that.

Mixed Hearing Loss - How To Treat It?

It is that time of the year when insects are all around. Suddenly one feels a buzzing sound or an itchy feel in the ear. To your horror, one feels a live insect is in your ear, which can be extremely annoying and is like a nightmare. Insects often get stuck when they enter our ears as they cannot fly or crawl out. They try to find their way out and their movements inside our ears can be very uncomfortable, painful and can be itchy as well. Moreover, they can easily produce infection.

In this scenario, do not try to remove an insect with cotton swab, tweezers or hair clip as it will make the situation worse and can lodge the insect deeper into the ear canal, which can possibly damag the eardrum, leading to permanent hearing loss. If an individual is not certain about the potential harm taht can be caused by the insect in the ear, one should seek medical care immediately. Insects in the ear are common reasons for visits to doctor's clinic, especially in children.

If one suspects an insect in ear, one may experience pain, swelling, blood or crackling. One may even feel biting, stinging, hearing loss or dizziness. It is best to stay calm in this situation as being active may lodge the bug further in ear or cause it to move further back or cause serious damage to the sensitive eardrum

One way to try to remove a bug in ear is by tilting the ear toward the ground and attempt to wiggle the ear. Grasp the earlobe and give it a wiggle. If the bug is not too far into ear canal, it may fall out on its own. If the bug is still alive and is not too far inside of the ear canal, it may simply come out on its own. If one stays calm and keep objects including fingers away from ears, it is likely that the bug will find its way back out of ear.

One can also try to flush the ear with warm water with a dropper or a bulb syringe. This can be done by holding head upright and stretching the ear canal by pulling the outer ear and then putting a steady stream of warm water into ear. Tilt head to the side to drain out the ear. Do not try this if one suspects that ear drum has been ruptured to prevent additional damage.

To avoid stinging or eardrum rupture from scratching or biting , one may use a drop or two of mineral, baby, or olive oil inside your ear canal to kill the insect. Finally, visit an ENT specialist doctor as they can remove the insect by special suction devices. Post insect removal, one must look out for signs of infection as swelling, dizziness, hearing loss, fever, and pain. Finally follow up with ENT specialist or Otolaryngologist for the final opinion.

How to Remove Insect from Ear at Home? 

What causes hearing loss? + How to ensure you can help it as you age

The partial or total inability to hear is known as hearing impairment or hearing loss. It can be present at birth, or develop later in life.

There are a number of factors, which may cause hearing loss

1. Age - Age is the biggest factor when it comes to the loss of hearing, and you may lose the ability to hear as you age. This condition is known as presbycusis. It becomes difficult to understand high-frequency sounds like that of a child or a woman when you get old.

2. Noise - When you are exposed to loud noises for a prolonged period of time, it damages your ears. This leads to loss of hearing. 5% of the total population of the world is affected by noise (the degree of suffering varies). It may be a result of continuous exposure to loud music or a sudden exposure to a loud noise like an explosion.

3. Hereditary disorders - Hearing disorder may be inherited by the dominant or recessive genes of parents in the child. 70-80% of these cases inherit from the recessive genes, whereas 20-25% inherit hearing loss from the dominant genes.

4. Trauma - Serious injuries of the head/ears may cause loss of hearing, which may be either temporary or permanent. When damage is caused to the brain, the brain fails to process the message conveyed by the ears. So even if the ears are totally functional, a person may face the problem in hearing.

5. Perinatal problems - The ototoxic effects on the fetus due to excess intake of alcohol during pregnancy lead to hearing the loss in about 64% of the infants born to alcoholic mothers.

Also, premature birth can be associated with hearing loss due to high risk of being exposed to noise in neonatal units.

Knowing about the causes of hearing loss can lead you a step closer to preventing this disorder as you age.

Here are some useful tips that can help prevent hearing loss:

1. Be more aware - You should be diligent and aware of the situations, which may risk your hearing ability and should try to avoid such situations as much as possible. Limit your exposure to sources of hazardous noises like firearms, firecrackers, concerts and clubs.

2. Take precautionary measures - If your occupation calls for working at an environment of loud noises, use earplugs or earmuffs to block out the excessive noise. Also, make sure that you work in a place where employers take all the necessary measures of noise control under the federal or state regulations.

3. Monitor your use of gadgets - Monitor and control the use of hearing devices, and try to reduce the use of headphones/ earphones as much as possible.



What causes hearing loss? + How to ensure you can help it as you age

A cochlear implant is an electronic device that is used to restore hearing ability in people who suffer from hearing loss due to inner ear damage. Unlike hearing aids which amplify sounds so people with hearing loss are better able to perceive them, cochlear implants directly transmit electronic sound signals to the auditory nerve. They work by compensating for damaged cochlea, the part of inner ear that converts sound waves into neural impulses which are perceived by the brain. 

A child who cannot hear will also never be able to speak. 
Inability to hear and speak puts a person at disadvantage in society. 
Simple tasks like talking on the phone which we take for granted become impossible. 
Conventional methods of learning like attending a classroom lecture become impossible. 
Brain development and intelligence is closely linked to development of speech and language. 
Inability of parents to communicate with child leads to emotional distancing. 
Integrating a hearing disabled person in to society becomes a frustrating experience for all involved. 
Cost of integration per capita in much higher when compared to cost of Cochlear Implant. 
Children with Cochlear Implants are fully integrated in society with normal hearing & speech. 
Children with Cochlear Implants can attend regular schools & colleges 
Early identification of hearing impairment gives children a better chance of developing speech and language skills, and of making the most of social and emotional interaction from an early age. 
Cochlear implants offer a multitude of benefits to people experiencing hearing loss, especially infants and children with severe hearing loss who are just starting to process language and speech. Some of these benefits are: 

Hearing and communication   Cochlear implants improve hearing significantly, especially to a level where normal communication can be restored. It enhances the person s ability to hear speech without relying on visual cues such as lip reading or hand signs. It makes telephonic conversation a lot easier. Cochlear implants also help people regulate their own voice and volume so that it is easier for others to understand them. 
Quality of life - It can help people with hearing loss listen to and enjoy music and also watch television with sounds. It helps people listen to sounds in a noisy environment and differentiate soft sounds from loud ones. 
Safety   Cochlear implants enhance the individual s safety as it allows the person to be able to hear warning sounds like honking cars or ambulance sirens. This will allow people to navigate public spaces in a much safer way. 
Society - For children with hearing loss, cochlear implants can help them adjust a lot better to regular schools instead of requiring special institutions. 
Brain development - It can help infants with cochlear damage develop their speech recognition and speaking skills much faster. 
Cochlear implants 

Only device of its kind that can restore a special sense.
Consists of 2 parts-
One part is surgically implanted in the body 
Second part is worn behind the ear and communicates with internal part using wireless signals 
Persons of any age can get a cochlear implant, from less than one year old children to 90 year old persons have received implants all around the world. 
Cochlear implants can be done for partial hearing loss also, know as Hybrid implant that preserves the residual natural hearing and augments hearing only in certain sound frequencies in which hearing loss is present. 
Are being used for indications other than hearing loss also like Tinnitus. 
Surgery is a day care procedure for most patients. 
Consult a doctor to get a clear assessment of whether you would be an eligible candidate for a cochlear implant and what to expect from the procedure.

Cochlear Implant - The Many Benefits Of It

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